Which of the following is TRUE about Tetralogy of Fallot?
A. Cyanosis is often present in the first few days of life.B. There is a right sided aortic arch in about 50% of cases.
C. The murmur becomes softer during a cyanotic spell as flow through the pulmonary valve is increased.
D. There is an association with DiGeorge syndrome
Ans. D. There is an association with DiGeorge syndrome.
Tetralogy
of Fallot is the most common congenital cyanotic heart condition. It may present
with cyanosis in the first few- of life, though this is rare. Usually it
presents as a murmur detected in first few months of life or as hypercyanotic
in late infancy. A hot bath will increase cyanosis, as the vasodilatation
results in a decrease in the peripheralvascular resistance, and so flow through
the pulmonary artery decreases, and cyanosis increases. During a cyanotic spell
the decreased not increase. flow through
the pulmonary artery results in the murmur becoming softer or inaudible. There
is a right sided aortic arch in about 30% of cases
